Systemic scleroderma is a rare connective tissue disease with significant orofacial consequences. Information on oral aspects of pediatric scleroderma is limited in the dental literature and current scientific evidence doesn't provide a differentiated approach to these patients. The proposed protocol was based on reference guidelines for pediatric dentistry and adjusted according to orofacial features observed during clinical evaluation of a child with systemic scleroderma. This project will provide a proper intervention of pediatric dentistry on approach of children with systemic scleroderma, contributing to oral and general health improvement of these special patients. Schlagwörter: Scleroderma, juvenile systemic sclerosis, systemic sclerosis, child, childhood, pediatric dentistry, oral manifestations